Juvenile xanthogranuloma - Voyaga Etmagan Ksantogranulomahttps://en.wikipedia.org/wiki/Juvenile_xanthogranuloma
Voyaga Etmagan Ksantogranuloma (Juvenile xanthogranuloma) gistotsitozning bir shakli bo‘lib, “Langergans bo‘lmagan hujayrali gistotsitoz” deb tasniflanadi. Bu kamdan‑kam uchraydigan teri kasalligi bo‘lib, birinchi navbatda bir yoshgacha bo‘lgan bolalarga ta’sir qiladi, lekin katta yoshdagi bolalar va kattalarda ham uchraydi. Lezyonlar to‘q sariq‑qizil dog‘lar yoki papulalar shaklida ko‘rinadi va odatda yuz, bo‘yin va yuqori magistralda joylashgan. Voyaga Etmagan Ksantogranuloma (juvenile xanthogranuloma) odatda olti oygacha bo‘lgan bolalarda bosh va bo‘yinning ko‘plab shikastlanishlari bilan namoyon bo‘ladi. Holat odatda bir yildan besh yilgacha o‘z‑o‘zidan yo‘qoladi. Tashxisni tasdiqlash uchun lezyonning biopsiyasi juda muhimdir.

Ko‘zning shikastlanishi JXG bilan kasallangan odamlarning 10 %ida namoyon bo‘ladi va ularning ko‘rish qobiliyatiga ta’sir qilishi mumkin. Teri lezyonlari odatda o‘z‑o‘zidan yo‘qolsa‑da, ko‘zning shikastlanishi kamdan‑kam hollarda o‘z‑o‘zidan yaxshilanadi va davolanishni talab qiladi.

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  • Bolalarda sariq nodullar. Oddiy voyaga etmagan ksantogranuloma (Juvenile xanthogranuloma)
References Juvenile Xanthogranuloma 30252359 
NIH
Juvenile xanthogranuloma (JXG) – bu juda keng tarqalgan holat bo'lib, bolalarda non‑Langerhans cell histiocytic disorder ning eng tez‑tez uchraydigan turidir. Taxminan 75 % hollarda bu lezyonlar hayotning birinchi yilida namoyon bo'ladi, va bemorlarning 15‑20 % dan ortig'i tug'ilishdan keyin paydo bo'ladi. Kattalarda kamdan‑kam hollarda JXG uchraydi; odatda yigirma yoshdan o'ttiz yoshgacha bo'lgan odamlarda kuzatiladi va kattalardagi bemorlarning ko'pchiligida faqat bitta lezyon mavjud. Klinik jihatdan u asosan yuz, bo'yin va tananing yuqori qismida bir yoki bir nechta sariq‑to'q sariq‑jigarrang qattiq bo'laklar yoki nodullar shaklida namoyon bo'ladi. Og'iz bo'shlig'ining shikastlanishi kam uchraydi, lekin tilning yon tomonlarida yoki og'izning boshqa joylarida sariq bo'lak shaklida paydo bo'lishi mumkin, bu esa yara va qon ketishiga olib keladi. Teri lezyonlari odatda simptomlarni keltirib chiqarmaydi va bir necha yil davomida o'z‑o'zidan o'tib ketadi. Kamdan‑kam bo'lsa‑da, ko'zning shikastlanishi teridan tashqari eng ko'p uchraydigan muammo bo'lib, keyin esa o'pka. Ocular JXG odatda faqat bitta ko'zga ta'sir qiladi va bemorlarning 0,5 % dan kamida uchraydi, ammo ko'z kasalliklari bilan og'riganlarning taxminan 40 % tashxis qo'yilganda bir nechta teri lezyoniga ega bo'ladi.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
 Juvenile Xanthogranuloma: An Entity With a Wide Clinical Spectrum 32721389
Juvenile xanthogranulomas (JXGs) keng tarqalgan non‑Langerhans cell histiocytoses toifasining bir qismi bo'lgan kam uchraydigan, yaxshi prognozli kasallikdir. Ular odatda bir yoki bir nechta qizil yoki sarg'ish bo'laklar shaklida namoyon bo'ladi, ko'pincha bosh yoki bo'ynida paydo bo'ladi. Ko'pgina JXGlar tug'ilish paytida yoki hayotning birinchi yilida rivojlanadi. G'ayrioddiy bo'lsa‑da, ba'zida ular teridan tashqaridagi joylarga ham ta'sir qilishi mumkin; mavjud adabiyotlarga ko'ra, ko'z ishtiroki ham kuzatilishi mumkin. Odatda, teridagi JXGlar o'z-o'zidan yo'qoladi va davolashni talab qilmaydi.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.